Hypocomplementemic urticarial vasculitis: report of a pediatric case
Identifieur interne : 002537 ( Main/Exploration ); précédent : 002536; suivant : 002538Hypocomplementemic urticarial vasculitis: report of a pediatric case
Auteurs : M. A. Cadnapaphornchai [États-Unis] ; F. T. Saulsbury [États-Unis] ; V. F. Norwood [États-Unis]Source :
- Pediatric Nephrology [ 0931-041X ] ; 2000-03-01.
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Abstract
Abstract : Hypocomplementemic urticarial vasculitis syndrome (HUVS) is well described in adults but is quite rare in children. We report a pediatric case of HUVS initially diagnosed as juvenile rheumatoid arthritis and then as Henoch-Schönlein purpura. Beginning at 3 years of age, our patient developed polyarthritis with hypocomplementemia. She subsequently experienced an intermittent purpuric rash beginning at age 4 years, and she continued to have episodic arthritis and rash for years. Hematuria and proteinuria were noted at 12 years of age; renal biopsy revealed membranoproliferative glomerulonephritis with membranous features. Serum complement evaluation revealed activation of the classical pathway, consistent with HUVS. Therapy with oral dapsone led to improvement in proteinuria. HUVS should be considered in the differential diagnosis of pediatric patients with glomerulonephritis, urticarial rash, arthritis/arthralgias, and obstructive pulmonary disease.
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DOI: 10.1007/s004670050770
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Norwood</name><affiliation wicri:level="1"><country xml:lang="fr">États-Unis</country><wicri:regionArea>Department of Pediatrics, University of Virginia Children’s Medical Center, Charlottesville, Virginia, USA</wicri:regionArea><wicri:noRegion>USA</wicri:noRegion></affiliation></author></analytic><monogr></monogr><series><title level="j">Pediatric Nephrology</title><title level="j" type="sub">Journal of the International Pediatric Nephrology Association</title><title level="j" type="abbrev">Pediatr Nephrol</title><idno type="ISSN">0931-041X</idno><idno type="eISSN">1432-198X</idno><imprint><publisher>Springer-Verlag</publisher><pubPlace>Berlin/Heidelberg</pubPlace><date type="published" when="2000-03-01">2000-03-01</date><biblScope unit="volume">14</biblScope><biblScope unit="issue">4</biblScope><biblScope unit="page" from="328">328</biblScope><biblScope unit="page" to="331">331</biblScope></imprint><idno type="ISSN">0931-041X</idno></series></biblStruct></sourceDesc><seriesStmt><idno type="ISSN">0931-041X</idno></seriesStmt></fileDesc><profileDesc><textClass><keywords scheme="KwdEn" xml:lang="en"><term>Glomerulonephritis</term><term>Key words Hypocomplementemia</term><term>Obstructive lung disease</term><term>Urticarial vasculitis</term></keywords></textClass><langUsage><language ident="en">en</language></langUsage></profileDesc></teiHeader><front><div type="abstract" xml:lang="en">Abstract : Hypocomplementemic urticarial vasculitis syndrome (HUVS) is well described in adults but is quite rare in children. We report a pediatric case of HUVS initially diagnosed as juvenile rheumatoid arthritis and then as Henoch-Schönlein purpura. Beginning at 3 years of age, our patient developed polyarthritis with hypocomplementemia. She subsequently experienced an intermittent purpuric rash beginning at age 4 years, and she continued to have episodic arthritis and rash for years. Hematuria and proteinuria were noted at 12 years of age; renal biopsy revealed membranoproliferative glomerulonephritis with membranous features. Serum complement evaluation revealed activation of the classical pathway, consistent with HUVS. Therapy with oral dapsone led to improvement in proteinuria. HUVS should be considered in the differential diagnosis of pediatric patients with glomerulonephritis, urticarial rash, arthritis/arthralgias, and obstructive pulmonary disease.</div></front></TEI><affiliations><list><country><li>États-Unis</li></country></list><tree><country name="États-Unis"><noRegion><name sortKey="Cadnapaphornchai, M A" sort="Cadnapaphornchai, M A" uniqKey="Cadnapaphornchai M" first="M. A." last="Cadnapaphornchai">M. A. Cadnapaphornchai</name></noRegion><name sortKey="Norwood, V F" sort="Norwood, V F" uniqKey="Norwood V" first="V. F." last="Norwood">V. F. Norwood</name><name sortKey="Saulsbury, F T" sort="Saulsbury, F T" uniqKey="Saulsbury F" first="F. T." last="Saulsbury">F. T. Saulsbury</name></country></tree></affiliations></record>Pour manipuler ce document sous Unix (Dilib)
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